Extraskeletal Ewing sarcoma – A deceptive entity on imaging

Geetha Ganesan; Thiagarajan  Veerappan; Kalpana Sivalingam

doi:10.5455/ajdi.20240322021817

Abstract
ABSTRACT
Background: Ewing sarcoma arising from soft tissue is referred to as an Extraskeletal ewing sarcoma (EES). It is a rare tumor that primarily affects young people and has an aggressive course with a high recurrence rate. Imaging findings of EES tumors are generally non-specific, with some variation based on location and the tissues involved.
Case summary: We present two rare cases of EES in adolescent females: one from the right kidney masquerading as renal cell carcinoma (case 1), and the other one primarily arising from the left chest wall (case 2).
Conclusion: EES, albeit rare, should be considered in patients with large, heterogeneous soft tissue masses. Radiologists should be aware of this deceptive entity because, despite its non-specific appearance, imaging can assist in determining tumor extent, surrounding infiltration, distant metastasis identification, surgical feasibility, and thus the best treatment options.

Key words: Key words : : Extraskeletal ewing sarcoma (EES), Renal cell carcinoma, Chest wall lesion